Prune belly syndrome

Alternative Names

Eagle-Barrett syndrome; Triad syndrome; Urethral obstruction malformation sequence

Definition of Prune belly syndrome

Prune belly syndrome is a group of birth defects that involve three main problems:

Causes, incidence, and risk factors

The causes of prune belly syndrome are unknown. The condition affects mostly boys.

Symptoms

Weak abdominal muscles can cause:

Signs and tests

A woman who is pregnant with a baby who has prune belly syndrome may not have enough amniotic fluid (oligohydramnios). This can cause the infant to have lung problems.

Treatment

Early surgery is recommended to fix weak abdominal muscles, urinary tract problems, and undescended testicles.

Expectations (prognosis)

Prune belly syndrome is a serious and often life-threatening problem.

Review

Luc Jasmin, MD, PhD, Departments of Anatomy and Neurological Surgery, University of California, San Francisco, CA. Review Provided by VeriMed Healthcare Network. Also reviewed by David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc. – 10/14/2009

ADAM Medical Encyclopedia

Article written by

A.D.A.M., Inc. is accredited by URAC, also known as the American Accreditation HealthCare Commission (www.urac.org). URAC's accreditation program is an independent audit to verify that A.D.A.M. follows rigorous standards of quality and accountability.