Progeria

Alternative Names

Hutchinson-Gilford syndrome

Definition of Progeria

Progeria is a disease that produces rapid aging, beginning in childhood.

Causes, incidence, and risk factors

Progeria is a rare condition that is remarkable because its symptoms strongly resemble normal human aging, but occur in young children.

Signs and tests

The signs include:

Treatment

There is presently no treatment for progeria.

Expectations (prognosis)

Progeria is associated with a short lifespan. The average patient survives to the early teens. However, some patients can live up to 30 years. The cause of death is usually related to the heart or a stroke as a result of the progressive atherosclerosis.

Review

Chad Haldeman-Englert, MD, Wake Forest University School of Medicine, Department of Pediatrics, Section on Medical Genetics, Winston-Salem, NC. Review provided by VeriMed Healthcare Network. Also reviewed by David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc. – 8/26/2009

Coronary artery blockage

ADAM Medical Encyclopedia

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