Hallervorden-Spatz disease

Alternative Names

Pantothenate kinase-associated neurodegeneration

Definition of Hallervorden-Spatz disease

Hallervorden-Spatz disease is a movement disorder that is passed down through families (inherited).

Causes, incidence, and risk factors

Hallervorden-Spatz disease usually begins in childhood.

Signs and tests

The doctor will perform a physical exam and ask questions about the patient’s medical history. It is important to get a complete medical and family history, since the condition can run in families.

Treatment

The goal of treatment is to control the symptoms. There is no specific treatment for Hallervorden-Spatz disease.

Expectations (prognosis)

Hallervorden-Spatz gets worse and damages the nerves over time. It leads to a lack of movement and often death by early adulthood.

Review

David C. Dugdale, III, MD, Professor of Medicine, Division of General Medicine, Department of Medicine, University of Washington School of Medicine; Daniel B. Hoch, PhD, MD, Assistant Professor of Neurology, Harvard Medical School, Department of Neurology, Massachusetts General Hospital. Also reviewed by David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc. – 9/28/2010

ADAM Medical Encyclopedia

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